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Table 1 Clinicopathological data of reported cases.

From: Primary pancreatic leiomyosarcoma: a case report

Case Number

Year

Author

Age/Sex

Clinical features

Morphological Findings

Clinical management & outcome

1

1951

Ross

80/M

Weight loss, mass, LUQ

Whole pancreas; wide spread metastases without lymph node involvement

Autopsy case

2

1956

Berman & Levene

47/M

Jaundice

Head of pancreas;5.5 cm; no metastases

Pancreatodudenectomy ; well 1 year later

3

1957

Feinberg et al

14/M

Epigastric pain; nausea

Head;11 cm; no metastases

Pancreatodudenectomy

4

1965

Becker et al

No data available

No data available

Cystic change

No data available

5

1970

Oyamada et al

47/M

General fatigue, mass, LUQ

15 cm

Nonresectable

6–10

1973

Baylor & Berg (5 cases)

51 (Median), M:3, F:2

No data available

Localized:1;Locally advanced:1;Disseminated:3

No data available

11

1976

Carda et al

56/F

Nausea & vomiting

Whole pancreas

Gastrostomy; died in 9 months

12

1981

Ishikawa et al

44/M

Epigastric pain, mass

Head;8 cm,; localized at operation

Pancreatodudenectomy; liver metastases 4 years later

13

1982

Tulha et al

28/F

Weight loss, mass

Head;20 cm

Pancreatodudenectomy ; Lung & liver metastases 15 months later

14

1990

Murata et al

55/F

No data available

Head & tail; no metastases

Caudal pancreatectomy

15

1991

Lakhoo & Mannell

68/M

Abdominal pain, weight loss, mass

Body;17 cm; no metastases

Distal pancreatectomy, gastric resection & transverse colectomy; well 2 years later

16

1993

De Alava et al

71/M

Abdominal pain, weight loss

Body;3.6 cm; no metastases

Pancreatectomy

17

1994

Peskova & Fried

68/F

Malena

Head;15 cm; localized

Pancreatodudenectomy;well 3 years later

18

1994

Sato et al

53/F

Abdominal pain, mass

Body;25 cm; no metastases

Distal pancreatectomy

19

1994

Ishii et al

66/M

Incidental finding

Tail;14 cm; wide spread metastases without lymph node involvement

Nonresectable

20

1995

Aranha et al

46/F

Epigastric pain, nausea, vomiting

Body;3 cm; localized

Distal pancreatectomy; dead in 9 months

21

1997

Owen et al

40/M

Abdominal pain

Head;6 cm; no metastases

Pancreatodudenectomy; well 10 year later

22

2000

Nesi et al

76/M

Fever

Tail;8 cm; localized

Distal pancreatectomy; dead in 12 months

23

2007

Present case

73/M

Weight loss, Epigastric pain, abdominal mass

Body;10 cm, hepatic metastases

Nonresectable; dead in 3 months